- primary immunodeficiency
- characterized by
- B and T cell abnormalities.
- associated with
- recurrent respiratory tract infections,
- can result in chronic lung disease.
- PAthology
- ILD with manifestations of
- pulmonary lymphoid hyperplasia (PLH),
- follicular bronchiolitis,
- lymphocytic interstitial pneumonitis (LIP), and
- nodular lymphoid hyperplasia.
- GLILD
- Granulomatous and Lymphocytic Interstitial Lung Diseases
- Radiologic evaluation
- variety of chronic pulmonary findings, including
- air trapping,
- bronchial wall thickening,
- bronchiectasis,
- emphysema,
- ground glass opacities,
- parenchymal consolidation,
- pulmonary nodules,
- scarring/fibrosis.
TCV
