60-year-old man with heart murmur since his teens, but recently became symptomatic with signs of right heart failure characterized by ankle edema, ascites and anasarca. Examination confirmed massive ascites and peripheral edema with RV hypertrophy and a coarse ejection systolic murmur in the pulmonic area and absent second heart sound (pulmonic valve closure)
CXR showed aneurysmal dilatation of the left pulmonary artery, decrease pulmonary vasculature, and calcification of the pulmonary valve, pulmonary annulus and tricuspid valve annulus. EKG showed RVH
At catheterization there was a 100 mm Hg gradient across the valve, mean right atrial pressure was 16 mmHg, RV systolic pressure was 120/24 mmHg and PA pressure 25/12 mmHg. Femoral artery O2 sat was 87.5%

CONGENITAL PULMONARY STENOSIS WITH ANEURYSMAL LPA, PV AND TRICUSPID ANNULUS CALCIFICATION

Ashley Davidoff MD

CONGENITAL PULMONARY STENOSIS WITH ANEURYSMAL LPA, PV AND TRICUSPID ANNULUS CALCIFICATION
The pulmonary valve is nodular and calcified (yellow) surrounded by a calcified pulmonary annulus (green), associated with a calcified tricuspid annulus (teal), and scattered calcification over or in the right ventricle (orange).

Ashley Davidoff MD

CONGENITAL PULMONARY STENOSIS WITH ANEURYSMAL LPA, PV AND TRICUSPID ANNULUS CALCIFICATION
RAO view of the heart shows a nodular and calcified  pulmonary valve (yellow) surrounded by a calcified pulmonary annulus (green), associated with a calcified tricuspid annulus (teal), and aneurysm of the LPA (blue)

Ashley Davidoff MD

CONGENITAL PULMONARY STENOSIS WITH ANEURYSMAL LPA, PV AND TRICUSPID ANNULUS CALCIFICATION
LAO view of the heart shows a nodular and calcified pulmonary valve (yellow) surrounded by a calcified pulmonary annulus (green), associated with a calcified tricuspid annulus (teal). The aneurysm of the LPA is not easily visualized in this view.

Ashley Davidoff MD

CLINICAL SUMMARY
CARDIAC CATH REPORT